Audio Clinical Professionals

Palatal Tremor and Myoclonus Dystonia

Explains hereditary essential myoclonus, an individual has nocturnal ear “clicking” and rhythmic palatal movements.., and palatal tremor in practical Movement Disorder care.

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Duration

00:03:04

File size

1.82 MB

Practitioner-Guided Note

When nocturnal clicking with rhythmic palatal movements is present, recognize palatal tremor as a structural posterior fossa disorder and look for a predisposing lesion along the Guillain-Mollaret triangle from trauma, multiple sclerosis, or stroke. In myoclonus dystonia with alcohol responsiveness, set realistic goals with pharmacotherapy—GHB, clonazepam, and divalproex may reduce but rarely abolish symptoms, and DBS can be considered in refractory cases.

Key Takeaways

Optimal treatment strategy for this condition is not explicitly specified in the source text; It most commonly develops in the wake of structural lesions that disrupt the dentate-red nucleus-inferior olive pathway, such as trauma, multiple sclerosis, or an ischemic stroke; This represents a palatal tremor, which was formerly known as palatal myoclonus, and it is often classified as an essential palatal tremor; Movements are notably exacerbated by emotional stress and caffeine intake, but they can be significantly improved with alcohol; Autosomal dominant disorder where myoclonus characteristically manifests before the age of twenty and presents right alongside an associated dystonia